Peroxisome aiki. Zellweger ciwo

Yau muna kiran ku zuwa la'akari peroxisome aiki. Abin da darajar da suka yi a cikin keji? mu ma da hankali ga abin da cutar za a iya gano tare da taimakon wannan organelle.

Tuni a cikin gabatarwa, a fili yake cewa da peroxisomes - shi da wasu gabbansa. A cell, bi da bi, wani bangare ne na wani wuce yarda da nagartaccen zanen dukkan abin da yake kẽwayenku mu. Ko mutumin da aka hada da Kwayoyin, wanda akwai manya-manyan lamba. Kuma da cell aka yi sama da ko da karami sassa, amma da suka ba ta daman yin kai mai zaman kanta rayuwa, wato, domin hada da haifar da sifofi ba lallai ba ne. Wani misali na wannan shi ne mafi sauki guda-celled halittu, wanda ka yiwuwa ji a ilmin halitta darussa a makaranta.

Kafin mu lissafa kuma bayyana peroxisome aiki, muna bukatar mu fahimci abin da shi ne da kuma yadda za su yi aiki.

peroxisomes

Wadannan wasu gabbansa bayyana a matsayin kankanin vacuoles, su size ne a kasa 1.5 micron. Peroxisome kewaye da wani bakin ciki membrane, kuma shi rarrabe microgranules ciki, daga ciki yanayi na gaba dayan cell. Abin da za mu iya samu a cikin organelle? Akwai da zuciyar, shi ne kuma ake kira da nucleoid. Yana da muhimmanci a gane cewa wannan bangare na peroxisomes yana da wani dangane da makaman nukiliya tsarin ko nucleoid kwayoyin. Kada dame waɗannan Concepts. kuma shi ne sau da yawa haka da cewa gano Tsarin mimicking lu'ulu'u nucleoid zone. Suna kafa daga fibrils da shambura. A core wannan organelle rabu da peroxisomes, uratoksidoza dauke a cikin ta. Wannan shi ne daya daga cikin enzymes. Yanzu mun ba da shawara a yi la'akari da peroxisome aiki a cikin cell. Amma kafin haka, a kusa look at tsarin.

tsarin

Yanzu za mu gaya abin da peroxisomes, tsarin da ayyuka (ga tebur) shi ma za a yi la'akari da mu. Don fara da mu ba a gani agaji a cikin wani nau'i na tebur. Next, rubuta fitar a daki-daki cikin tsari da kuma aiki na peroxisomes. Tebur za a iya halitta ta da mu, amma Isar da shi zuwa bayanin kula da cewa peroxisome matrix kuma kunshi wani nucleotide.

Matrix 15 ƙunshi peroxisome enzymes. Bari mu dubi wasu. Nuna rubutu mafi muhimmanci daga cikinsu suna:

• peroxidase.
• catalase.
• oksidoza.
• uratroksidaza.

Kuma abin da aiki sai ya aikata wani nucleotide? Its rawa ne to cunkoso wadanda wannan enzymes. Bari mu dubi ga aiwatar da kafa peraksisom. Su toho daga EPS, saboda haka muna iya cewa yankin na samar da wannan organelle - a CSE. Enzymes ake samar a cikin:

• EPS.
• hyaloplasm.

Ga shi yana da muhimmanci ga bayyana da cewa da membrane, ko bakin ciki, amma shi ba ya shiga har cikin ions kuma a low kwayoyin nauyi substrates. Yanzu za mu iya la'akari da aiki na peroxisomes. Somin-ta ~ wannan organelle shi ne na bayar da muhimmanci ga cell.

ayyuka

Peroxisome ayyuka ne kamar haka:

• hadawan abu da iskar shaka da kwayoyin abubuwa.
• m acid hadawan abu da iskar shaka.
• biosynthesis plasmalogens.
• isoprenoid biosynthesis a cikin dabbobi;
• biosynthesis na cholesterol.
• NDR2 gina jiki sarrafawa.
• tsari na tsari kumburi.
• taimako a cikin aiwatar da numfasawa a shuka Kwayoyin, da sauransu.

Wannan jerin sosai tsawon, saboda wasu ayyuka suna ba tukuna cikakken gane. Yanzu muna bayar da kadan more magana game da gina jiki kira. Yana da muhimmanci a san cewa wadannan da wasu gabbansa dauke da sassa kamar:

• DNA.
• ribosome.

Haka kuma, gina jiki kira auku a tsakiya. Next ne shigo da na ciki yanayi na peroxisomes. Ta yaya core na shigo? By halartar C-m sigina. A jerin wannan niyya ne sosai takaice, kunsha na 3 amino acid sharan.

The darajar a asibiti jarrabawa

Mun gani a baya sashe, wanda aikin da aka yi da peroxisomes. Yanzu kadan game da asibiti data manufa organelle. Yanzu muna magana kadan game da cutar da ake kira - Zellweger ciwo. Wannan shi ne quite wani tsanani cuta, shi ne ya sa ta a take hakkin gina jiki shigo. Saboda haka, peroxisomes komai, tantanin halitta da kuma kwayoyin a matsayin dukan gano data m gazawar wasu gabbansa. Mutane suka sha wahala daga wadannan cuta da wahala da aikin wasu muhimmanci jikuna a nan sun hada da:

• kwakwalwa.
• hanta.
• kodan.

Yara suka haifa tare da wannan ciwo ba zai iya rayuwa mai dogon lokaci da kuma ake tilasta su bar mu duniya bayan wani sosai short tsaya. Cutar da ake dangantawa da maye gurbi na organelle. Shi ne kuma zai yiwu da kuma kasa m siffofin da cutar.