Eisenmenger ciwo: Haddasawa, Alamun, ganewar asali, Jiyya

A cardiology a general kuma a nakasar malformations musamman a wannan lokacin da akwai riga dubun "maras" yanayi. Wasu daga cikin su suna bayyana na dogon lokaci da kuma nasarar bi a ante- da neonatal lokaci, amma mafi har yanzu neman mai bincike. Daya daga cikinsu shi ne Eisenmenger cuta. A ciwo da aka gano a cikin farkon karni na ashirin da mashawarta Austria pediatrician kuma yanzu Bears sunansa.

definition

Eisenmenger ciwo (Eisenmenger) - wannan take hakkin Natal ci gaban da zuciya tsoka, wanda ya hada da kasancewar wani aibi a cikin septum tsakanin ventricles, da lakã otzerkalennoe matsayi da kuma kara girman da dama ventricle. Abin farin, wannan lahani za a iya samu nasarar, da kuma yara kara girma da kuma ci gaba a cikin wannan hanya kamar yadda da takwarorinsu.

statistics

A lokacin, game da biyar bisa dari na duka lokuta na cardiac anomalies a yara daukan Eisenmenger ciwo. Nakasar zuciya cuta za a iya raba da sauran cututtukan zuciya da na jarirai da kuma kananan yara. Wasu likitoci sun hada untreated wani hemodynamic disturbances a cikin wannan ciwo.

Syndrome ko hadaddun

Ware raba hadaddun da Eisenmenger ciwo. Syndrome - wani nadi uncorrected take hakki na wurare dabam dabam na jini ka kewaye da ci gaban tsakanin cavities na zuciya ventricles. A hadaddun hada da takamaiman cuta samu a cikin tayin ko jariri.

etiology

A tsari na yadda wannan ciwo ne kafa, har sai karshen ne ba a sani ba, masana kimiyya da kuma likitoci har yanzu kokarin samun wani bayani. Duk da haka, da suka gudanar quite da kyau, don su bincika dalilai saboda wanda Eisenmenger hadaddun bayyana. A dalilan za a iya raba biyu Categories: ciki, ko kwayoyin, da kuma waje, ko muhalli effects.

1. Magana game da wani kai tsaye hereditary watsa da wannan cuta ba zai iya zama, amma idan wani first- ko biyu-line dangi ne ba disturbances na samuwar muhimmanci gabobin, akwai ko da yaushe wani damar cewa yaro suka bayyana.
2. Guba a lokacin antenatal lokaci. A hadarin category hada da mata masu ciki a manyan birane, aiki a m aiki ko rubutu da sinadaran ko ta jiki gurɓatawa.
3. Shan magunguna. Wasu kwayoyi hatsari ya dauki a lokacin haihuwa. Saboda haka, kafin ganewa ko a farko makonni bayan da obstetrician ya kamata a yi shawara da duk samu kudi. Ko da shi ke nan kawai da ciwon kai Allunan.
4. A amfani da bitamin da kuma sinadirai masu kari na dubious quality. Yawancin wadannan abubuwa ne m, amma a rare lokuta da za su iya haifar da lalacewar da liyafar bai riga ya kafa kwarangwal na da yaro ko ya ciki gabobin.
5. A gaban daya daga cikin iyaye-to-dogon lokacin da kullum cutar.

Hakika, wadannan dalilai ba nuna musamman a kan Eisenmenger ciwo. Bayyanar cututtuka, ta bincike da kuma magance aka tattauna a kasa.

pathogenesis

Idan mutum yana da irin wannan sifofin ne ba, tabbata za a disturbances a jini wurare dabam dabam. Saboda gaban gagarumin na ramin zuciya septal aibi, kazalika sabõda zãluncin da matsayi na lakã ne gauraye venous da aortic jini a zuciya kogo. Watau kafa shunt da shunt daga hagu zuwa dama. A kan lokaci, da matsa lamba a cikin huhu akwati ƙaruwa, wani lokacin shi yiwuwa ko da wuce waɗanda suke a cikin lakã. Wannan, bi da bi, take kaiwa zuwa wani reflex spasm na kananan jini a cikin huhu wurare dabam dabam. Tasowa na huhu hauhawar jini. Idan shi yana mai dogon lokaci, to, akwai a compensatory thickening daga cikin ganuwar capillaries da jini stasis auku a cikin huhu.

Clinicians shared "fari" da "blue" Eisenmenger ciwo. A farkon yanayin, da shunt ne a cikin classic version, wato, daga hagu zuwa dama, da kuma a karo na biyu - a kan m.

cututtuka

A jarirai da kuma yara matasa musamman sanarwa cututtuka ne da wuya. Jiki da kuma ilimi ci gaban yara ba sha. Idan shekaru bayyana gaban shunting, sa'an nan da mutum shortness na numfashi, blue nasolabial alwatika da extremities, gajiya, palpitations ko arrhythmia palpable zafi na angina irin. Hankula ne halin da ake ciki da cewa marasa lafiya dauki don rage bayyanar cututtuka - squatting. Saboda haka ya zama sauki numfashi.

Da na kowa ailments iya ji sau da yawa gunaguni na ciwon kai, nosebleeds, kuma coughing sama da jini. Za ka iya canza murya saboda matsawa na jijiya endings na arteries dilated. Sau da yawa wanda za su iya tsayar da pathologies kamar protrusion daga cikin kirji irin hump da kuma canja m phalanges na yatsunsu kamar yadda drumsticks, nuna cardiopulmonary gazawar, wanda ake kira Eisenmenger ta ciwo. Haddasawa, cututtuka, ganewar asali sanar da kowane likitan zuciyar.

A hadaddun iya wuya ta mashako, ciwon huhu, endocarditis kwayan etiology, zubar da jini daga cikin huhu, da kuma ko su ciwon zuciya. Ba tare da lura, da rayuwar jama'a a adam marasa lafiya ne ba fiye da shekara talatin.

bincikowa da

Abin baƙin ciki, a lokacin da Talakawa jarrabawa bayyanãwa da cutar ba zai yiwu. Domin tabbatar da presumptive ganewar asali, bukatar musamman da hanyoyin da bincike:

1. X-haskoki daga cikin kirji, wanda zai nuna na gani canji na zuciya contours da manyan tasoshin.
2. Angiography mũnãnan ayyuka kamar Dabarar dabara na jijiyoyin bugun gini ci gaban da ake amfani da sau da yawa, amma a wannan yanayin shi ne ba musamman, da kuma iya kawai gane canje-canje sosai gogaggen gwani.
3. ECG m, a wannan lõkacin, idan shi ne aka gudanar karkashin Holter saka idanu. Sa'an nan da bayanai likita ba zai zama da minti biyar Taruwa, kuma ga cikakken rana, kuma ya za su iya gane canje-canje a cikin sha'awa kudi.
4. Echocardiography - duban dan tayi na zuciya ne. An kyau kwarai hanya domin ganowa lahani a cikin cavities na zuciya da jini cuta.
5. Cardiac catheterization, a cikin wannan harka - mafi m ne kuma abin dogara Hanyar bincike. Ya taimaka wajen gane duk lahani, sanin da halaye na guda zuciya da kuma samar da magani.

Wannan irin wannan da wuya a gane asali Eisenmenger ciwo. Alamun (cuta magani multistage da kuma lokaci-cinyewa) ta nonspecific Pathology ne ya ɓadda a matsayin na kowa cuta da kuma tsere hankalin general practitioners.

magani

Duk da har abada adawa tsakanin likitoci da kuma likitoci, a cikin hali na wannan cuta, sun amince da cewa kokari bukatar da za a bi a matsayin ra'ayin mazan jiya magani a kanta ba ya ba da ake so sakamako, kuma m ba zai iya samar da barga gafarta musu. Saboda haka, a sa na matakan da aka tsara don kawar da Eisenmenger ciwo:

1. Jinni (tare da wani zamani karkatarwa, wannan ne ake kira "phlebotomy"). Simple da kuma matsala-free wajen. Ana amfani da marasa lafiya da Pathology tabbatar da kamar wata sau a shekara. Kafin da kuma bayan hanya dole ƙaddara da da danko jini da kuma haemoglobin matakin.
2. Amfani da inhaled oxygen. Amfani da matsayin adjunct far wa magance cyanosis da hypoxia sakandare. Bugu da kari, suna da wani psychosomatic sakamako a kan marasa lafiya.
3. Anticoagulants. Su ba su da wani isasshen matakin na shaida kamar yadda zai yiwu a samu daga cikin frying kwanon rufi a cikin wuta, kuma maimakon jini thinners don samun ta da cikakken nesvorachivaemost.
4. Sauran magunguna:
   - diuretics for cire huhu edema.
   - mafita don inganta hemodynamics.
5. M dabara:
   - pacemaker rama domin arrhythmia.
   - cikakken kau na wani na ramin zuciya septal aibi ƙulli kuma wani mahaukaci shunt.

Daidai yadda za mu bi Eisenmenger ciwo ya kamata a magance da likita ko ma da dama da kwararru. Saboda haka yadda za a ba da wani garanti na nasara ba zai iya zama wani daya Hanyar.