Kiwon lafiyaCututtuka da kuma Yanayi

Thrombocytopenic purpura a manya: ganewar asali, haddasawa da kuma magani

Thrombocytopenic purpura a manya - shi ne mai cuta da za a iya kai wa ga m zargin manyan bruises da kuma zub da jini. Matsayin mai mulkin, da jini da asarar ne saboda da m fall a platelet count - Kwayoyin cewa taimaka wajen clotting.

Wasu kafofin wannan Pathology kuma ake kira rigakafi thrombocytopenia. Ana rinjayar biyu manya da yara, amma a cikin matasa marasa lafiya kamar yanayin yawanci tasowa a bango na wani kwayar cutar da ke kawo a kan kansa ba tare da bukatar musamman da magani. A manya, cutar ne a mafi yawan lokuta wani dogon daya.

Idan kana da wani alamu na zub da jini da kuma platelet ƙidaya, ko low, amma, bisa manufa, m, likita zai fi yiwuwa ba za rubũta magani. A rare lokuta, duk da haka, yawan platelets da dama zuwa wani m m, haddasa rai-barazanar ciki zub da jini. Domin lura da wadannan rikitarwa bukatar likita nan da nan baki.

cututtuka

Thrombocytopenic purpura a manya (hoton sama) ne ko da yaushe tare da waje bayyananen cuta. A cikin hali na hankula cututtuka su ne wadannan alamun cutar:

  • ma m samuwar manyan bruising (hematoma).
  • na waje zub da jini a cikin fata cewa kama wani kurji na kankanin, ja-m aibobi (petechiae) da aka sarrafa da mafi yawa a kan kafafu.
  • zub da jini daga gumis ko hanci.
  • gaban da jini a cikin fitsari ko stool.
  • unusually nauyi hailar zub da jini.

Lokacin da ganin likita

Thrombocytopenic purpura a manya iya zama wani tsanani damuwa, kuma a wannan yanayin shi ne mafi alhẽri ka sanya wani wa'adi a gaba ga wata m gwani.

Idan ka fara jinni, kira "motar asibiti." Hankula ga wannan cuta zub da jini ba za a iya sarrafawa da al'ada wajen daga gida kit ko hankula hanyoyin da jini ya kwarara Tashoshi. Alal misali, za ka ba taimake jiki matsa lamba a kan dace yanki na jiki. Masana sun bayar da shawarar juya don taimakon likitoci maza maza.

dalilai

Idiopathic thrombocytopenic purpura a manya wani lokacin tasowa domin jiki ta rigakafi da tsarin kuskure hare-hare, kuma ya halaka platelets. Kalmar "idiopathic" na nufin "wadda aka fitar ga wani ba a sani ba dalili". thrombocytopenia haka faye hali a lokuta inda likitoci da ikon sanin abin da jawo rashin dauki na rigakafi da tsarin.

The yara saita bango Pathology ne yawanci sauki, tun da cuta ya zama mafi yawa daga wani cutar (mumps ko mura). An zaci cewa da kamuwa da cuta disrupts da al'ada aiki na rigakafi da tsarin.

Kara platelet Lalacewar

Idan da farko ganewar asali zama thrombocytopenic purpura a manya, da asibitin (asibiti manifestations) an haɗa, yawanci tare da wani rigakafi cuta. A antibodies hašawa zuwa platelets, sa alama su kamar yadda Kwayoyin da za a hallaka. Saifa tsara don magance waje cututtuka, da antibody gane da kuma kawar da platelets daga jiki. A sakamakon wannan erroneous fitarwa a jini circulates yawa karami yawan platelets a kwatanta da na kullum.

Al'ada platelet kirga Range daga 150 zuwa 450 dubu Kwayoyin da microliter na zagawa da jini. Mutane bincikar lafiya tare da "thrombocytopenic purpura" (manya) analysis bayyana kawai 20,000 Kwayoyin bukata. Tun platelets inganta jini clotting, Munã rage adadin su na kara hadarin zub da jini da kuma ciki zub da jini. A matakin na 10 dubu cell farauto. Tare da irin wannan gagarumin raguwa a yawan platelets ciki hemorrhage m fara har ma ba tare da wani rauni.

hadarin dalilai

Thrombocytopenic purpura a manya (Photo amfani a farkon wannan labarin, ya nuna da waje bayyananen cuta) da aka samu a kowane zamani, duk da haka, masana kimiyya sun gano biyu hadarin abubuwan da ƙara da alama bunkasa cutar bayyanar cututtuka. Su ne:

  • Jima'i ainihi. A mata, wannan cuta da aka yi fama a kan talakawan biyu zuwa sau uku fiye da sau da yawa fiye da maza.
  • Kwanan nan, wani kwayar cutar. Mumps, kyanda da kuma na numfashi cututtuka na iya haifar da bayyanar da halayyar bayyanar cututtuka na thrombocytopenia, amma dangantaka da ƙwayoyin cuta sami mafi sau da yawa a cikin yara.

Yana yi taƙawa da hadarin rikitarwa. A mafi tsanani daga gare su - da wannan ne a kwakwalwa hemorrhage, wanda zai iya zama m.

ciki

Ko da yake thrombocytopenic purpura a manya kamu har a mata masu juna biyu, da matsayi na jariri kiwon lafiya irin Pathology uwa a mafi yawan lokuta ba ya canzawa. Masana, duk da haka, shi ne shawarar duba matakin na platelets a cikin jini da jariri nan da nan bayan haihuwa.

Idan ka kasance ma'abũta ciki, amma gwajin da sakamakon nuna wani karu a platelet count, kai ne a hadarin da yiwuwar wani karfi bude zubar hemorrhage ne sosai high. A irin haka ne, akwai wani likitan mata ko asibiti, likitoci kamata tattauna tare da ku da samuwa hanyoyin kwantar da hankali ne hadari ga yara.

bincikowa da

Likita ya iya yin wani cikakken ganewar asali "thrombocytopenic purpura" (manya), ganewar asali ya kamata a yi a kan bambanci manufa. Ya kamata a nan da nan sarauta daga sauran yiwu Sanadin zub da jini da kuma rage yawan platelets - msl, kullum cututtuka ko illa da kwayoyi dauka da ku.

A gwani zai tambaye ku tambayoyi game da kiwon lafiya da tarihin, za su samar da farko likita jarrabawa da kuma za designate daya ko fiye da misali bincike gwaje-gwaje. A karshen sun hada da:

  • Complete jini count. Bisa wani samfurin dauka daga wani haƙuri ta jini aka ƙaddara sauran rabo na da maikacin jini, da kuma musamman yawan platelets. Lokacin da thrombocytopenia karshe siga ne abnormally low, duk da cewa da matakan da farin da kuma ja da maikacin jini zai zama ga talakawan.
  • Clinical bincike na jini. Wannan binciken da aka sau da yawa ya yi su tabbatar da matakin na platelets samu ta hanyar total jini analysis. A haƙuri misali aka sanya a kan wani musamman gilashin nunin da kuma nazari a karkashin wani hange.
  • Analysis na bargo. Wannan bincike Hanyar ne kawai bada shawarar ga adult marasa lafiya da suka gabata ganewar asali "thrombocytopenic purpura" (manya mayar da martani ga irin wannan taron shi ne mafi isasshen, su ne sauki ga jure wa hanya).

Platelets aka samar a cikin bargo - da taushi, spongy nama, a tsakiyar manyan ƙasũsuwa. A wasu lokuta, likita zai iya cire wani samfurin na kashi nama located shiga cikin bargo biopsy Hanyar. Wasu kwararru fi son dauki samfurori for analysis ta wata hanya da ake kira "ɗammãni," sa'an nan cire daga bargo kawai wani sashi daga cikin ruwa bangaren. Mafi sau da yawa, biyu hanyoyin da ake yi a lokaci guda kuma suna tare kira "bargo analysis."

Idiopathic thrombocytopenic purpura bargo ne free daga pathologies, kamar yadda raguwa a platelet ƙidaya lalacewa ta hanyar rushewa daga cikin sel a cikin jini da kuma tabarbarewa daga cikin baƙin ciki, kuma babu matsaloli tare da samar da platelets.

magani

Easy thrombocytopenic purpura a manya, da Sanadin wanda ba dogara kafa, yawanci ba ya bukatar takamaiman magani - quite a kai a kai gani da wani likita, kuma daga lokaci zuwa lokaci don duba matakin na platelets. Yara kusan ba ya bukatar magani, da kuma takaici gudanar da kanta. Manya, duk da haka, na iya bukatar wani tasiri magani idan da yanayin da ya zama mai tsanani ko tsawo (na kullum) hali.

Hanyar na far ne daban-daban da kuma bambanta daga magani girma inganta platelet count kafin tiyata don cire baƙin ciki (splenectomy). A bu mai kyau zuwa tattauna tare da likita a gaba magani zabin tare da amfani ko rashin amfani da aiki. Wasu marasa lafiya sami cewa illa daga shan magunguna cece su more damuwa da rashin jin daɗi fiye da ainihin sakamakon da cutar.

magunguna

Likita zai tattauna tare da ku da illa da kuma sashi na magunguna da kuma abin da ake ci kari cewa kana shan a wannan lokacin. Zai yiwu wasu daga cikinsu taimaka wajen rage matakan platelets a zagawa da jini. Wadannan illa da asfirin, "Ibuprofen", "Ginkgo biloba" da "Warfarin".

Babban jerin

Lokacin da ganewar asali aka tabbatar da "thrombocytopenic purpura" a manya, magani iya kunshi shan wadannan magunguna:

1. magunguna da cewa kashe da na rigakafi da tsarin. Mutane da yawa marasa lafiya a farkon far sallami baka corticosteroids kamar "Prednisone". Rage rigakafi da tsarin aiki, wannan magani inganta platelet count. Da zarar batutuwan ya isa wani m matakin na, zai kasance karkashin kulawa na likita hankali daina shan magani. A hanya na lura daukan daga biyu zuwa shida makonni.

Matsalar shi ne cewa thrombocytopenic purpura a manya, da bayyanar cututtuka na wanda ya zo da kõme ba, bayan samun "Prednisone" iya dawo a karshen far. Doctors yawanci rubũta wani sabon Hakika na corticosteroids, duk da haka, wannan magani ba za a iya ci gaba da ganin wani ƙarshe saboda tsanani gefen sakamakon wannan magani irin. Idan zai yiwu yawan abin sama cataract, ya karu da jini sugar matakan, ƙãra hadarin cututtuka da kuma osteoporosis (weakening na da ƙasũsuwa).

2. Allura don kara jimlar yawan jini Kwayoyin. Idan corticosteroids ba taimaka, likitoci rubũta allura, na rigakafi da globulin. Wannan magani ana amfani a lokuta inda haƙuri saukar tsanani zub da jini da bukatar nan da nan m baki. A sakamako yana for mako biyu. Daga cikin yiwu illa - ciwon kai, amai, da kuma low jini.

3. formulations hanzarta platelet samar. Kwayoyi kamar "Romiplostim" da "Eltrombopag" ( "PROMAKTIV"), na taimaka da bargo, don samar da karin platelets. A cikin irin illa iya zama ciwon kai, dizziness, tashin zuciya da kuma amai.

4. Sauran immunosuppressants. "Rituximab" ( "Rituxan ') rage tsanani da mahaukaci martani na rigakafi da tsarin wanda results a cikin wani al'ada platelets hallaka. Damar illa hada da fata rash, low jini, zazzabi, da kuma ciwon makogwaro.

Idan kwayoyi ne m

Idan (da kuma wani lokacin ba taimake a adult abinci mai gina jiki a bisa tsarin da lafiya salon, da guje wa barasa da kuma shan magani don rabu da matsala) ka ci gaba thrombocytopenic purpura, wani likita na iya bayar da shawarar tiyata. Kau da baƙin ciki (splenectomy) hanzari gusar da Pathology, kamar yadda Likita cuts da babban hallakar da platelets. Ka tuna ko da yake, cewa za ku zama a hadarin postoperative rikitarwa. Bugu da kari, mutane ba tare da wani baƙin ciki kullum a wani ƙãra hadarin ƙulla cututtuka.

madadin hanyoyin

Idan, domin kiwon lafiya, ko sauran dalilai, ba za ka iya iya tiyata, da gwani na iya rubũta da m na sabon magunguna - misali, "azathioprine" ( "Azathioprine", "Azasan"). Duk da haka mafi m kwayoyi unsa mafi tsanani illa. "Azathioprine", musamman, yana sa wani karuwa a jikin zazzabi, ciwon kai, tashin zuciya da amai, da tsoka zafi.

Tare da kullum zagi

Kana kamu da "thrombocytopenic purpura"? A manya, abin da ya faru da wannan cuta na bukatar wani canji a salon. Tun da cutar tare da wani ƙãra hadarin zub da jini, kauce wa yiwuwar hatsari lamba wasanni (dambe, Martial Arts, kwallon kafa) da kuma yadda za ka iya kula da jikinsa.

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