Kiwon lafiya, Cututtuka da kuma Yanayi
Marmara kashi cuta: haddasawa, cututtuka, magani, yin rigakafi
Marmara ne a nakasar cuta Pathology cewa an bayyana ta yaxuwa osteosclerosis mafi kwarangwal ƙasũsuwa da zurfin canje-canje a cikin alli-phosphorus metabolism. A cuta ne musamman rare. An farko aka bayyana a cikin shekara ta 1904 ne Jamus likita da radiologist Albers-Schoenberg (Albers-Schonberg NE). Marmara cuta na faruwa gaba daya a duk shekaru Categories, a kasashe a duk faɗin duniya, daidai a duka biyu mata da maza.
Haka kuma cutar tana da yawan ma'ana - nakasar osteosclerosis, osteopetrosis, kuma dysplasia giperostaticheskaya Albers-Schonberg cuta. Kada gauraye marmara cutar da wani ciwo da ake kira "marmara fata." Lokacin da marmara kashi cuta a cikin kwarangwal fara nuna karin m abu, kazalika a medullary canal fara ci gaba da wani m kashi. A marmara kira nakasar fata vazonevroz tasoshin a cikin fata, mafi sau da yawa abin da ke faruwa a cikin yara da kuma bayyana kanta reticular spots a kan fata a bluish launi bayan quenching. Bayan jin wuta da alama vuya. Yana kuma na faruwa a manya marmara fata da bakin ciki haske fata da suke da matsaloli tare da jini.
A etiology da wannan cuta ne ba a sani ba. A mafi sani lokuta da cutar yana da wani marmara iyali harafin da ake daukar kwayar cutar daga tsara zuwa tsara. Sunansa marmara cuta gare musamman hoto na X-haskoki na kwarangwal, wanda aka denoted da wani sabon abu homogeneity da kuma kaifi kashi yawa, kazalika da rashin kashi tsarin. Da alama cewa kasusuwa ne Ya sanya daga marmara.
Akwai biyu siffofin da cutar marmara:
- gudãna ba tare da wani bayyane asibiti bayyanar cututtuka, kamu kawai ta X-ray jarrabawa.
- bayyana kanta a farkon yara, ya furta bayyanar cututtuka.
Babban alama da cuta ne da ci gaba da ko m hardening na trabecular kashi. A can farko da cutar kawai sclerotized tubular ƙasũsuwa a cikin kashi metaphyses da lebur a gefe rabo. Bugu da ƙari kuma, gano unequal hatimi girman kwanyar kashi, sun fi mayar da abin ya shafa paranasal rami, musamman firamare da frontal. Shan kashi ne ma fallasa da kuma jawbones, shi yana tare da take hakkin da shigowa da kuma hakori ci gaba - canza su tsari,} arancinsu Tushen, obliterating da tashoshi da cavities na hakori. Mafi sau da yawa marasa lafiya neman magani hanyar zafi a cikin wata gabar jiki da kuma gajiya a lokacin tafiya. Marmara kashi cuta ma adversely rinjayar da ci gaban da jijiyoyin bugun gini tsarin, kamar yadda wuce kima girma na mahaukaci kashi nama sannu a hankali ya sauya hematopoietic nama.
Best sakamakon cutar zalunta marmara da aka samu a yunkurin transplants (transplants) bargo. Lalle tasiri lura da wannan cuta ba a halin yanzu wanzu. Jiyya da wannan cuta da aka yafi da nufin karfafa murdede da kuma juyayi tsarin, da kuma dauki a mafi yawan lokuta kamar yadda sauran asibitoci. Marasa lafiya nuna physiotherapy, tausa kuma yin iyo. Abinci mai gina jiki ya zama wani cikakken, arziki a abubuwan da alama bitamin, dole ne su kasance ba a menu, cuku, nunannun 'ya'yan itatuwa da kayan lambu,' ya'yan halitta da kuma kayan lambu juices. Yara tare da wannan ganewar asali lokaci zuwa lokaci aika zuwa sanatorium magani.
Ainihin hanyoyin domin hana cutar marmara da dangantaka rike perinatal bincike gestation 8 makonni. Don hana abin da ya faru na kashi nakasar da kuma pathological samu karaya kamata a da za'ayi tsauri Nazarin a orthopedics.
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