Ectodermal kuma fibrous dysplasia. koda dysplasia

Karkashin dysplasia (fassara daga Girkanci kamar yadda dys - musu. Wplasis - ilimin) yana nufin ba daidai ba, kuma dõmin karkatarwa da ci gaban da wani sashin jiki. Wannan shi ne - a gama lokaci rufe wani take hakki.

Fibrous dysplasia tana nufin cututtuka na kwarangwal tsarin, da kuma halin a cewa kashi nama aka maye gurbinsu fibrous nama. Wannan tsari deforms da ƙasũsuwa. Babban dalilin wannan cuta ne bayyanar da ƙari tsari, wanda zai fara a cikin yaro, sa'an nan ya fara ci gaba. Fibrous dysplasia ne yawanci a mata.

cuta da dama sukayi fassara. Mafi na kowa naúrar ne, dangane da matakin na yaduwa daga wani pathological tsari:

• monoossalnaya fibrous dysplasia rinjayar daya kawai kashi.
• poliossalnaya - canje-canje suna lura a mahara ƙasũsuwa (yawanci shimfidawa a gefe daya na jiki, kuma sau da yawa yakan faru a cikin shimfiɗar jariri).

A farko nau'i na cutar rinjayar da girman kwanyar kashi, da ruwa, tubular ƙasũsuwa (dogon) baki. Na biyu - a lokaci guda fiye da hamsin bisa dari na duka, ƙashi na daga cikin kwarangwal.

Babban rikitarwa hada da m samu karaya, abin da sauri coalesce, amma waye, iri a cikin ƙasusuwansa, kazalika da sarcoma.

Fibrous dysplasia zuwa wani magani ba zai iya zama, iya kawai orthopedic hanyoyin (dashi kashi curettage, osteotomy), da kuma nada kwayoyi da sauqaqa zafi.

Ectodermal dysplasia yalwaci babban yawan cututtuka da kuma syndromes (game da 100), jigon wanda yake gaban mahaukaci cin gaban Kalam ectoderm. A farko alamar - gaban hyperthermia, wanda a lokacin da ya bayyana, kuma m harin iya kai wa ga wani warwarewarsu wani ilimi ci gaba, ko mutuwa.

Zaka iya zaɓar da wadannan iri da su bayyanar cututtuka.

Angidroticheskaya fara bayyana kanta a jarirai, wani yaro da kuma ci gaba cikin rayuwa. Babban fasali su ne:

• hereditary cututtuka.
• karfi nakasawa da hakora.
• kasancewar wani slowdown a cikin kusoshi.
• mucosal atrophy (makogwaro, baki, hanci).
• da waje bayyanar shi ne kama da yaro marasa lafiya da ciwon nakasar syphilis.

Symptomatic aka ba da jiyya. Haramta: holidays a kudancin kasashen, aikin a zafi da kuma sinadaran da tsire-tsire.

Gidroticheskaya ekzodermalnaya dysplasia ne halin da canje-canje a cikin itãcen dabĩnai, soles, gashi ci gaba. Kamar yadda magani mafi yawa ana gudanar da bitamin "A" m da baƙin, softening tsami da kuma keratolytics. Bugu da kari ga wannan, yi amfani da: enzymatic nufin Methyluracilum, anabolic steroids, tutiya, amino acid da kuma biostimulants.

Koda dysplasia yana da dama iri cewa ya bambanta:

• morphological bayyananen (cystic da sauki).
• Sarrafawa (cortico-medullary, medullary da cortical).
• ruwan dare - total, segmental, mai da hankali).

Babban dalilin wannan cuta ne a kayyade abubuwan da teratogenic ciki da waje tasiri a amfrayo. Saboda haka, tushen da cuta ne nakasar malformations, wanda, ko da kuwa da irin, kai zuwa wani karu a koda size, mugun cin gaban parenchyma, wani gagarumin raguwa na ta ayyuka.

Jiyya da wannan cuta ne symptomatic kuma m lokuta idan akwai nuni ga dasawa da sashin jiki.

A general, dysplasia qunshi wani rukuni na cututtuka wanda ya unsa mahaukaci cin gaban wani sashin jiki ko dukan tsarin. Matsayin mai mulkin, babban Yanã - kwayoyin da nakasar dalilai.

Jiyya ne symptomatic, ko shawarwari ne ga wani sashin jiki dashi ko kashi.