Mẽne ne - wani ciwo Rokitansky-Otto Küstner? Syndrome Rokitansky-Otto Küstner: haddasawa, cututtuka, magani

Surrogacy damar yara mata da suka ga kiwon lafiya dalilai ba zai iya yi ciki yaro a kan nasu. Su bisa ga yawan adadin da statistics, ya karu daga shekara zuwa shekara. Daya daga cikin dalilan da roko ga sabis na wani surrogate uwa ne Rokitansky-Otto Küstner ciwo. A Sanadin cutar, da cututtuka da kuma asali hanyoyin magani da za a tattauna a wannan labarin. Za ka kuma koyi ko a mace tare da wannan ciwo suna yara.

Pathology halayyar

Syndrome Rokitansky-Otto Küstner-Meyer-Hauser - a rare gynecological cuta. ƙunshi sunayen masana kimiyya suka gabatar da wani cikakken bayanin irin Pathology a cikin sunan. Har ila yau a cikin likita adabi akwai ma'ana da cutar: farji atresia, aplasia na mahaifa. Duk da haka, ba su gani duk keta a cikin jiki, hali na ciwo. Bugu da ƙari, ta farji atresia iya faruwa saboda kumburi ko tiyata. Sau da yawa, da cikakken suna da cutar don rage farko biyu sunayen masana kimiyya ko da kalmar "MRKH ciwo".

A Pathology ne halin da cikakken ko m babu ya zauna cikin mahaifa, kazalika da 2/3 daga cikin farji. A wannan yanayin, akwai cikakken ci gaban da ovaries kuma al'aurar. Har ila yau adana sakandare jima'i halaye (jiki gashi a kan mace irin, kirji). Rokitansky-Otto Küstner ciwo ne suka kamu da wuya (daya hali da dubu 5. Girls jarirai).

tarihi bayanai

A farko kwatancin da cutar kwanan baya a 1829 shekara. Jamus likita Carl Mayer lura da cewa farji aplasia ne sau da yawa tare da wani iri-iri na cin gaba munanan. A kadan daga baya, a 1838, a sani akan cututtuka daga Austria Karl von Rokitansky ciwo bayanin kara. Ya ƙaddara cewa idan da wannan cuta ne ma ba a nan mahaifa, ovaries amma riƙe da ikon aiki da cikakken. A 1910, da Jamusanci likita Jamus Kyustner takaita da samuwa bayani a kan cutar, ya kara da ita kansa lura. Likitan ya bayyana misalai m hade tare da aplasia igiyar ciki malformations koda ci gaba. A shekarar 1961, Farfesa Zhorzh Hauzer daga Switzerland da shawarar cewa Kalmar "Otto Küstner Rokitansky-Mayer-ciwo". Scientist wallafa yawa lura da marasa lafiya tare da wannan ganewar asali, wanda kusantar da hankali ga insensitivity to namiji hormones tsakanin marasa lafiya. A 1977, Houser farko gabatar da wani bayanin da atypical bambance-bambancen da Pathology. Ganin manyan taimako na masana kimiyya, da ciwo da aka mai suna a gare discoverers na hudu sunayen.

Sanadin cutar

Ko da a cikin zamanin tayi zai kare fetal aza ilimin Halittar Jiki lahani cewa faye hali Otto Küstner-Rokitansky ciwo. Photos of yara tare da wannan ganewar asali bayan haihuwa ba ya bambanta da na su lafiya takwarorina. A cewar Muller ka'idar, tayin jima'i gabobin ci gaba a lokacin da watan biyu bayan ganewa. A tasiri na korau dalilai a kan jikin wani ciki a wannan lokaci zai iya sa cututtuka daban-daban a cikin yara. A kan abin da ya faru na wani ciwo kuma rinjayar connective nama dysplasia tayin a cikin abin da tashin hankali na da tsarin faruwa. Pathological canje-canje kai ga ci gaban m gabobin, daya bayyana abin da yake cikin Otto Küstner-Rokitansky ciwo.

Abin da abubuwan da tasiri da ya faru na da cuta a cikin jariri a lokacin daukar ciki?

1. Strong toxicosis.
2. HIV a cikin mahaifiyarsa.
3. A hatsari na zubar da ciki.
4. Shan wasu magunguna (kamar corticosteroids).
5. Barasa zagi.

A ciwo ba classified a matsayin hereditary cututtuka. Duk da haka, a asibiti yi akwai lokuta inda Pathology kamu da dama mata na wannan iyali.

Clinical manifestations da cutar

Otto Küstner-Rokitansky ciwo an fara don bayyana a cikin mafarki a lokacin da akwai mafarki kwayoyin. A 'yan mata hankali taso keya ƙirãza, da canza adadi, akwai jiki gashi a cikin m yankunan. Furta sakandare jima'i halaye ba da damar da ake zargi da kiwon lafiya da matsaloli. Mutane da yawa 'yan mata ji lokaci-lokaci sha raɗaɗin a cikin ƙananan ciki yankin, wani nauyi a cikin ƙananan baya. Duk da haka, da rashi na haila take kaiwa zuwa nemi taimako daga wani likitan mata. Wani dalili domin ziyara zuwa wani gwani na iya zama matsala na wani m yanayi. M yunkurin jima'i sau da yawa haifar da rauni da perineum ko katsewa na mafitsara. Bayyanuwar underdevelopment gawarwakin iya zama a matsayin rudimentary mahaifa da mahaukaci fallopian shambura. Aƙalla 40% na gaskiya jima'i MRKH ciwo a hade tare da malformations na urinary tsarin.

rarrabuwa na cututtuka

Kamar sauran anomalies na da amfrayo ci gaba, Rokitansky-Otto Küstner ciwo yana da daban-daban digiri na tsanani. A tsanani kowane daga cikinsu ne m da tsananin fetal munanan. Akwai uku siffofin da cutar:

1. Hankula MRKH ciwo (64% na duk lokuta). An halin aplasia na zauna cikin mahaifa, kuma farji.
2. Atypical MRKH ciwo (24% na duk lokuta). A wannan cuta, da 'yan mata bace mahaifa da farji, akwai wani tabarbarewa na ovaries.
3. MURCS-ƙungiya (12% na duk lokuta). Wannan shi ne mafi tsanani nau'i na ciwo, wanda aka halin cuta da aka jera a sama da aka complemented wani mahaukaci ci gaban da kwarangwal.

Form da cutar kayyade warkewa dabarun da kuma taimaka likitoci yi Hasashen na dawo.

hanyoyin da ganewar asali

Abin dubawa shi ne wajibi ne don tabbatar da ciwo Rokitansky-Otto Küstner? Alamun cutar ba ne kawai rarrabẽwa ga ganewar asali. haƙuri jarrabawa ta fara da wani gani dubawa. A 75% na lokuta, shi, ba Ya bayyana wani take hakki, saboda sakandare siffofin dace norms. Sa'an nan, wata rajistan shiga a kan gynecological kujera. A 'yan mata tare da bata da wannan fatar ganewar asali ne da za'ayi ta hanyar gabansa. Domin hankula short farji ciwo (2 har zuwa cm), wanda ba shine karshen da cervix tashar. Wani bincike zaɓi ne na rectal jarrabawa, a lokacin da likita Bincikar fallopian tube da kuma igiyar ciki rami. Wannan hanya ya sa ya yiwu don kimanta mataki na samuwar gabobin.

Regular ji na muhimmi da zazzabi taimaka ƙayyade lokaci na hailar sake zagayowar don tabbatar da cikakken aiki na ovaries. Bugu da kari, likita ya furta jini gwaje-gwaje domin hormones, MRI da pelvic duban dan tayi. A musamman tsanani lokuta na iya bukatar laparoscopic ganewar asali.

Hanyar magani

Akwai ne kawai hanya daya warkar da Rokitansky-Otto Küstner ciwo - m roba. Operation a kan samuwar cikin farji kira colpopoiesis zuwa ta kula da likitoci sun koma ga XIX karni. Da farko, da aiki amfani da su bi mata da kiyaye mahaifa ayyuka. A cikin wadannan marasa lafiya da jini bai zo ba daga jiki, da kuma a hankali tara a cikin kogon ciki. A sakamakon haka, da suka da aka kamu da neoplastic matakai, wanda aka tare da ciwo mai tsanani da kuma daban-daban da rikitarwa.

A halin yanzu rike colpopoiesis hanyoyi biyu:

1. Fadada daga cikin farji da taimakon wani inflatable balan-balan. The aiki daukan lokaci mai tsawo. Its aiwatar mai yiwuwa ne kawai idan farji tsawon ba kasa da 4 cm.
2. Formation neovaginy rabo daga sigmoid ciwon ko fata na ciki. Modern fasahar tozartar gyara lahani ba tare da ciki incisions - laparoscopically. Likitoci sun fi son wannan hanya, da samuwar wani wucin gadi farji.

Manufa shekaru domin colpopoiesis ne lokacin daga 16 zuwa shekaru 21. Wannan lokaci, karshe maturation da kwayoyin. Da nufin ta farji roba - taimaka mata don a ji dadin cikakken jima'i rayuwa. Don hana ta imperforate kamata ba bari na yau da kullum jima'i, lokaci-lokaci wuce bougienage hanya.

Matsalolin bayan tiyata

Mene ne rikitarwa bayan tiyata iya haɗu da marasa lafiya da ganewar asali "Rokitansky-Otto Küstner ciwo"? Jiyya da cutar ne, wani lokacin tare da wani m sakamakon. Colpopoiesis - wannan shi ne wani tsanani aiki. Kamar yadda da wani nau'i na tiyata, shi ne zai yiwu a ci gaba da rikitarwa. Daga gare su, ya fi na kowa ne sepsis da peritonitis. Har ila yau, da yawa marasa lafiya bayan wata hanya na lura, da likitocin da suka kamu da Fusion neovagina katangu. Wannan Pathology tasowa saboda rashin yau da kullum jima'i rayuwa. Saboda haka, likitoci karfi bayar da shawarar cewa mata ba su yin sakaci jima'i.

Forecast bayan dawo da

Canje-canje a cikin jiki da faruwa a mata da ganewar asali "Rokitansky-Otto Küstner ciwo" bai ba da damar a gudanar da haihuwa aiki a wani halitta hanya. Duk da haka, hanyoyin zamani na IVF da surrogacy taimako irin wannan marasa lafiya da nazarin halittu yara. Masana kimiyya sun kwanan nan sanar da sakamako mai kyau na mai bayarwa mahaifa dashi yadda ake gudanar. Bayan wani lokaci, watakila, dasawa na jiki zai taimaka mata tare da wannan insidious cuta a kan nasu to kai yara.

Rashin haihuwa da kuma ciwo Rokitansky-Mayer-Otto Küstner

Zan iya samun yara tare da wannan cuta? Wannan tambaya taso daga mata da yawa da suka fuskanci Pathology. Jima ko daga baya, kõwane ɗaya daga cikinsu yana so ya gwadawa a kan rawar da mahaifiyarsa. Mafi yawan mata tare da wannan ciwo ba zai iya kai yaro. Idan ovaries suna aiki kullum, don haka masana bayar da shawarar marasa lafiya yi tunani akai da sabis na surrogate mahaifiyarsa. A wannan yanayin da jariri da aka ɗauki cikinsa?

A mataki na farko a surrogate uwa shirin da m mace an wajabta hormonal kwayoyi. Da amfani da kwayoyi a cikin wani lokaci ba ka damar aiki tare da su hailar hawan keke. Sai matar ta kwai ciwo MRKH artificially inseminated da maniyyi daga mijinta. Cikin 'yan kwanaki da suka "girma" a cikin matsakaici da cewa mimics da kaddarorin da fallopian shambura. Bayan kwanaki uku, masana suna fara pre-kafawa shiri: ƙayyade da jima'i da tayi, gaban chromosomal lahani kuma hereditary cututtuka. A rana ta biyar ta samo asali tayi da aka canjawa wuri zuwa cikin mahaifa na wani surrogate mahaifiyarsa. A wasu lokuta, a biyu podsazhivanie, misali, a kan uku da kuma rana ta biyar.

Yawan tãyuna canjawa wuri su iya bambanta dangane da ingancin da kwayoyin abu, shekaru na haƙuri. A fatawar da mace, da sauran kwai sha cryopreservation hanya. A sakamakon wannan ganewa a cikin duniya a 9 months akwai wani m baby. Duk da haka, wannan hanya yana da biyu magoya bayan da kuma abokan adawar.

Dabam kamata la'akari da surrogacy. A yawa na musamman kananan dakunan shan magani a can ne ake kira mata tushe, wanda suke son a samar da wani irin sabis. Yawancin lokaci shi ne matasa, da lafiya da 'yan mata. Daya daga cikin dalilan da resorting to irin wannan asibitin ne a ciwo Rokitansky-Otto Küstner-Meyer-Hauser. Hotuna gaba surrogate uwãyensu kuma za a iya samu a cikin wannan database. A dukan tsari, daga zabin da wani m biomamy da kuma kawo karshen ciki, iko cibiyar shugabanninsu ba. Saboda haka shi ne mafi kyau a tuntube da masana, maimakon shiga a cikin search for kai. Kawai a cikin wannan hanya na iya zama m, a nan gaba kiwon lafiya na baby.

don takaita

Syndrome Rokitansky-Mayer-Otto Küstner - shi ne mai kwayoyin cuta halin rashi ko hypoplasia na zauna cikin mahaifa, kuma farji. Mutane da yawa 'yan mata kafin balaga ba su ma san game da kiwon lafiya da matsaloli. Amenorrhea sa su su ga likitan mata. Sai a wata liyafar a gwani suka farko zama sane da wanzuwar irin wannan wani ciwo. A daya hannun, shi ne na hali to maldevelopment na zauna cikin mahaifa, kuma farji, da kuma a kan sauran - gaban sakandare jima'i halaye. Yau, akwai da dama da magani zabin ga cututtuka. Dukan su suna kullum ana inganta da kuma supplemented. A far da cuta ne a cire aibi da m robobi. A sakamakon haka, da mãsu haƙuri iya rabu da mu da rai da physiological matsaloli, more rayuwa da kuma ko da suna da yara. Game da karshen aya, shi na bukatar taimako na wani surrogate mahaifiyarsa.